A Case of Combined Intrahepatic Portosystemic Shunt, Midgut Malrotation, and Renal Rotational Anomaly in an Adult Patient
نویسندگان
چکیده
rare condition, except for cases of a dilated paraumbilical vein caused by portal hypertension, (1). Also, a midgut malrotation is rare in adulthood with a reported incidence of 0.2% (3). Midgut malrotation is usually an isolated abnormality, but it can be associated with congenital heart disease or situs problems (4). But, to our knowledge, there are no reports of associations of both abnormalities with kidney malrotation. We report, for the first time, a case of intrahepatic portosystemic shunt combined with midgut malrotation, and a renal rotation anomaly in a 44-year-old woman.
منابع مشابه
Abernethy malformation associated with Caroli’s syndrome in a patient with a PKHD1 mutation: a case report
BACKGROUND Abernethy malformation is a rare congenital anomaly characterised by the partial or complete absence of the portal vein and the subsequent development of an extrahepatic portosystemic shunt. Caroli's disease is a rare congenital condition characterised by non-obstructive saccular intrahepatic bile duct dilation. Caroli's disease combined with congenital hepatic fibrosis and/or renal ...
متن کاملAsymptomatic Congenital Intrahepatic Portosystemic Shunt
Congenital (spontaneous) intrahepatic portosystemic shunt is rare in the English literature. Most cases of portosystemic shunt occur after trauma, surgery, liver biopsy or as a result of chronic portal hypertension. Chronic shunting may result in encephalopathy, bleeding or hyperinsulinism. We report a case of an asymptomatic adult female with a presumed congenital intrahepatic portosystemic sh...
متن کاملCongenital Intrahepatic Portosystemic Venous Shunt and Liver Mass in a Child Patient: Successful Endovascular Treatment with an Amplatzer Vascular Plug (AVP)
A congenital intrahepatic portosystemic shunt is a rare anomaly; but, the number of diagnosed cases has increased with advanced imaging tools. Symptomatic portosystemic shunts, especially those that include hyperammonemia, should be treated; and various endovascular treatment methods other than surgery have been reported. Hepatic masses with either an intra- or extrahepatic shunt also have been...
متن کاملCT-assisted transfemoral intrahepatic portosystemic shunt in a long duration follow-up: A case report
BACKGROUND Transjugular intrahepatic portosystemic shunt (TIPS) in patients with portal hypertension may be considered as a rescue therapy in case of recurrent variceal bleeding or failure of endoscopic management. CASE REPORTS We present a case of a patient with massive gastroesophageal variceal bleeding refractory to numerous endoscopic treatments in which TIPS was considered in an attempt ...
متن کاملAdult Midgut Malrotation with Ladd’s Band: a Rare Case Report with Review of Literatures
Background: Midgut malrotation is an anomaly of intestinal rotation that occurs during fetal development and usually presents in the neonatal period. It is rare for midgut malrotation to present in adulthood. Method: We present a case of 15 year old girl presenting with acute abdomen of 15 days duration. Clinical evaluation and investigations revealed features of acute small gut obstruction wit...
متن کامل